Clinical course and characterisation of lymphangioleiomyomatosis in a Brazilian reference centre.

201433 citationsJournal Article

Authors

Bruno Guedes Baldi · Hospital das Clínicas da Faculdade de Medicina da Universidade de São Paulo

Genival Fernandes de Freitas

Mariana Sponholz Araújo

Olívia Meira Dias

Daniel Pereira

Suzana Pinheiro Pimenta

Ronaldo Adib Kairalla

Carlos Roberto Ribeiro de Carvalho

Abstract

Clinical and functional features of the LAM patients from our centre are similar to those from other countries. Our sample showed preserved exercise capacity, with desaturation in the 6MWT, and impaired quality of life. Survival was similar, whereas the annual rate of decline of FEV1 was slightly lower than in recent studies.

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Publication Details

Published in: PubMed

Volume 31, Issue 2, pp. 129-35

Field-Weighted Citation Impact: 2.04

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Clinical course and characterisation of lymphangioleiomyomatosis in a Brazilian reference centre.

Authors

Abstract

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Publication Details