Management of acute metabolic decompensation in maple syrup urine disease: A multi-center study

199936 citationsJournal Article

Authors

Makoto Yoshino · Kurume University

Kikumaro Aoki · Kagawa Nutrition University

Hideki Akeda · Naha City Hospital

Kazuko Hashimoto

Tetsuo Ikeda · Kumamoto City Hospital

Fumio Inoue · Kyoto Prefectural University of Medicine

Michinori Ito · Tokushima University

Abstract

Therapeutic goals to improve neurological outcome are to shorten the duration of the altered level of consciousness, and to minimize the peak plasma leucine level as much as possible.

Topics & Keywords

Metabolism and Genetic Disorders Alcoholism and Thiamine Deficiency Biochemical and Molecular Research

UN Sustainable Development Goals

Good health and well-being

Publication Details

Published in: Pediatrics International

Volume 41, Issue 2, pp. 132-137

DOI: 10.1046/j.1442-200x.1999.4121044.x

Field-Weighted Citation Impact: 0.43