Primary glomus tumor of the kidney

Primary glomus tumors of the kidney are rare with only 33 cases reported in the literature. We present a 59-year-old lady with abdominal pain and dyspepsia with a provisional diagnosis of renal cell carcinoma on imaging. Pathological examination revealed a mesenchymal pericytic tumor with morphology and immunohistochemistry being most consistent with malignant glomus tumor. We believe this is the first case of glomus tumor of the kidney in the Indian literature. We report this case given its rarity and to add to the existing published data.