Global frequency, diagnosis, and treatment of hereditary angioedema with normal C1 inhibitor

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Authors

Markus Magerl · Humboldt-Universität zu Berlin

Marc A. Riedl · La Jolla Institute for Immunology

L. Karla Arruda · Clinics Hospital of Ribeirão Preto

Andréa Carla Bauer · University Hospital Carl Gustav Carus

Alejandro Berardi

Jonathan A. Bernstein · Bernstein Clinical Research Center

Laurence Bouillet · Université Grenoble Alpes

Abstract

HAE-nC1INH may be more prevalent than previously reported. Importantly, our findings revealed varying diagnostic and treatment approaches. Validated, accessible diagnostic biomarkers and clinical outcomes derived from rigorous clinical trials assessing mechanistically based treatments would advance understanding and management of HAE-nC1INH.

Topics & Keywords

Coagulation, Bradykinin, Polyphosphates, and Angioedema Vitamin K Research Studies

Publication Details

Published in: Journal of Allergy and Clinical Immunology Global

Volume 4, Issue 3, pp. 100446-100446

DOI: 10.1016/j.jacig.2025.100446

Field-Weighted Citation Impact: 11.97

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Global frequency, diagnosis, and treatment of hereditary angioedema with normal C1 inhibitor

Authors

Abstract

Topics & Keywords

Publication Details