Primary Intracranial Ewing’s Sarcoma of the Right Frontoparietal Region: A Rare Case Report

A BSTRACT Ewing’s sarcoma (ES) is a malignant tumor arising from the bones and soft tissues in children and young adults. However, primary intracranial ES is extremely rare, and they generally present as supratentorial or intraparenchymal tumors. There are no standard treatment guidelines for such cases, with each patient being managed on a case-by-case basis. This paper reports a case of a 15-year-old female patient who presented with a complaint of headache and vomiting. Radiology suggested an intracranial mass in the right frontoparietal region with thinning of the adjacent overlying bone. She underwent right frontal craniotomy with tumor excision, which, after histopathological examination and immunohistochemistry, showed features consistent with ES. She was managed with multiagent chemotherapy.